L-Phenylalanine CAS: 63-91-2 99% budada cad
Lambarka buugaagta | XD90317 |
Magaca Alaabta | L-Cysteine hydrochloride anhydrous |
CAS | 63-91-2 |
Qaanuunka molecular | C9H11NO2 |
Miisaanka Molecular | 165.19 |
Faahfaahinta Kaydinta | Ambient |
Xeerka Tarifka La Iswaafajiyay | 29224985 |
Tilmaamaha Alaabta
Muuqashada | Budada crystalline cad |
Qiimayn | 99% |
Wareegid gaar ah | -20.4 ilaa -35.2 |
Biraha culus | <0.002% |
Hogaamin | <10mg/kg |
pH | 5.4 - 6 |
Khasaare xagga qallajinta | <0.40% |
Hadhaaga dabka | <0.10% |
Cudurada kaadida maple sharoobada (MSUD), silsilad L-amino (BCAA) iyo 2-oxo acids (BCOA) waxay ku ururaan dareeraha jirka taasoo ay ugu wacan tahay yaraanta la dhaxlo ee silsilad laalaabtay 2-oxo acid dehydrogenase hawlo adag.Gudaha MSUD, macluumaad yar ayaa laga helayaa muhiimada ay leedahay in kaadida la tuuro xeryahooda silsilado laamood ah.Waxaan baarnay nadiifinta kelyaha ee leucine, valine, isoleucine iyo alloisoleucine, iyo 2-oxo acids 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S)-(S- KMV), iyo (R) -3-methyl-2-oxopentanoate (R-KMV), iyadoo la adeegsanayo lammaane balaasma iyo muunado kaadi ah (n = 63) oo laga keenay 10 bukaan oo qaba MSUD classical.Soo saarista kelyaha ee jajabka ah ee BCAA bilaashka ah waxay ku jirtay qiyaasta caadiga ah (<0.5%) oo ka madax bannaan uruurinta balaasmaha.Soo saarista xidhxidhan (N-acylated) BCAA waxay ahayd mid caadi ah oo aan si weyn ugu xidhnayn uruurinta balaasmaha BCAA.Soo saarista kelyaha ee jajabka ah ee BCOA waxay u kala horreysey KIC << KIV